Alpha 1-antitrypsin deficiency

Original article


Eriksson S, Elzouki AN.

Department of Medicine, Malmo University Hospital, Sweden.

Baillieres Clin Gastroenterol. 1998 Jun;12(2):257-73.


Alpha 1-Antitrypsin deficiency (PiZ) is frequent in Caucasian populations. The predominant clinical correlates of this inborn error, i.e. chronic liver disease, emphysema, and vasculitic syndromes including their pathogenetic background are discussed in the present review.

Keywords: Alpha 1-antitrypsin deficiency